During surgery, the heart surgeon removes the area of dissection or aneurysm. Due to the connective tissue disorder, the aorta is prone to tearing, so the heart surgeon must use great care.

A mechanical valve, attached to the end of the aortic graft, is sewn to the annulus (opening) of the aortic valve.

The coronary arteries are reattached to the aortic graft through small buttonholes cut into the graft. Then, the other end of the dacron graft is sewn to the tissue of the aorta.